Cor triatriatum with mitral stenosis: A diagnostic dilemma

Cor triatriatum sinister presenting in the adult as mitral stenosis.

Cor triatriatum sinister is a rare congenital defect in which the left atrium is divided by a fibromuscular membrane into two distinct chambers. Classically, patients present in infancy although in some cases they remain asymptomatic until adulthood. The clinical features on presentation can mimic those of mitral stenosis due to the obstructive properties of the membrane. Cor triatriatum sinist...

Cor triatriatum with pericardial agenesis.

Cor triatriatum: congenital stenosis of the common pulmonary vein.

Cor triatriatum is the term given to a rare congenital abnorTnality of the heart in which a septum separates what is apparently one of the atria into upper posterior and lower anterior chambers. With few exceptions, the septum has always been present on the left side of the heart. Other names given to the same anomaly naturally reflect the authors' views concerning the nature and origin of the ...

Cor triatriatum sinister.

C triatriatum is a very rare congenital cardiac anomaly with no known associated genetic abnormalities. Cor triatriatum is generally an isolated anomaly but may be associated with anomalous pulmonary venous return in approximately 10% of patients, patent ductus arteriosus, left superior vena cava, ventricular septal defects, Shone syndrome, tricuspid atresia, Ebstein malformation, atrioventricu...

Cor triatriatum sinistrum. Diagnostic features on cross sectional echocardiography.

M mode and cross sectional echocardiography was carried out in three cases of cor triatriatum sinistrum (two infants and one adult). In two cases a peculiar double arch appearance, not previously reported, was found. All three cases were referred for surgery without cardiac catheterisation, and the diagnosis proved to be correct. The characteristic echocardiographic feature of cor triatriatum i...